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Journal of Orofacial Orthopedics / Fortschritte der Kieferorthopädie

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01.07.2014 | Case Report

Dental and craniofacial characteristics in a patient with Hutchinson–Gilford progeria syndrome

verfasst von: Dr. C. Reichert, L. Gölz, W. Götz, M. Wolf, J. Deschner, A. Jäger

Erschienen in: Journal of Orofacial Orthopedics / Fortschritte der Kieferorthopädie | Ausgabe 4/2014

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Abstract

The Hutchinson–Gilford progeria syndrome (HGPS) is an exceptionally rare medical disorder caused by mutations in the lamin A/C gene. Affected patients display typical features of premature aging. Beside general medical disorders, these patients have several specific features related to the craniofacial phenotype and the oral cavity. In this article, the dental and craniofacial characteristics of a 9-year-old girl with HGPS are presented. It is the first report addressing orthodontic tooth movement and microbiological features in a HGPS patient. We describe and discuss pathologic findings and provide a detailed histology of the teeth which had to be extracted during initial treatment.

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Titel: Dental and craniofacial characteristics in a patient with Hutchinson–Gilford progeria syndrome
verfasst von: Dr. C. Reichert
L. Gölz
W. Götz
M. Wolf
J. Deschner
A. Jäger
Publikationsdatum: 01.07.2014
Verlag: Springer Berlin Heidelberg
Erschienen in: Journal of Orofacial Orthopedics / Fortschritte der Kieferorthopädie / Ausgabe 4/2014
Print ISSN: 1434-5293
Elektronische ISSN: 1615-6714
DOI: https://doi.org/10.1007/s00056-014-0216-x

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Dental and craniofacial characteristics in a patient with Hutchinson–Gilford progeria syndrome

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